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ICD-10-CM Sequencing Guidelines

  • Vijayarani Sivakumar
  • Published On - May 20, 2020

    Certain diagnosis codes in ICD-10-CM are not accepted as a principal or first listed diagnosis. Coding conventions defined in the ICD-10 manual describe these scenarios. The term “principal diagnosis” is used on inpatient facility claims and “first listed diagnosis” is used on outpatient and professional claims. The term “primary diagnosis” will be used in this document to refer to either.

     

    Etiology/Manifestation. Certain conditions have both an underlying etiology and multiple body system manifestations. Coding conventions require the condition be sequenced first followed by the manifestation. Wherever such a combination exists, there is a “code first” note with the manifestation code and a “use additional code” note with the etiology code in ICD-10. In most cases, the manifestation code will have “in diseases classified elsewhere” in the code title.

     

    Example: L62 -Nail disorders in diseases classified elsewhere

    Code first underlying disease, such as: Pachydermoperiostosis (M89.4)L62 is not accepted as a primary diagnosis because instructions require the underlying condition be coded first.

     

    In addition to the ICD-10 manifestation designation, CMS identifies manifestation codes for the Outpatient Code Editor. The CMS manifestation codes may not appear as primary diagnoses on outpatient hospital claims. CMS updates this list quarterly.

     

    What does “code first” mean?

    There are certain conditions that have instructional notes in the ICD-10-CM tabular/coding conventions that guide the coder in sequencing. This is especially true when the condition has a common manifestation or underlying conditions of a chronic disease. If there is a “code first” note in the tabular, the coder should follow this instruction and sequence the underlying etiology or chronic condition first followed by the manifestation as an additional diagnosis. There will be a “use additional code” note at the etiology/underlying condition.

     

    Another thing to look for is in the code title of specific diagnoses “in diseases classified elsewhere”. This part of the title is telling the coder that this is a manifestation code and is never permitted to be sequenced as the PDX or first listed code. When coders see a code in brackets this indicates that this code should not be sequenced first.

     

    Sequelae of Injuries. The residual or late effect of an injury generally requires two codes. The primary diagnosis must describe the nature of the sequela. The secondary diagnosis describes the original injury and usually has an “S” in the 7th position to indicate sequela. (Sequela of cerebrovascular disease is an exception.)

     

    Example: treatment of ankle instability following a sprain:

    M24.271 -Disorder of ligament, right ankle

    S93.411S -Sprain of calcaneofibular lig., right ankle, sequela

    S93.411S is not accepted as a primary diagnosis because instructions require the residual condition be coded first.

     

    Multiple Coding for a Single Condition. There are some single conditions that require more than one code. Coding instructions in the ICD-10 manual clearly indicate which must be coded first.

     

    Examples:

    K52.1 -Toxic gastroenteritis and colitis

    Code first (T51-T65) to identify toxic agent 

    Z16. -Resistance to anti-microbial drugs

    Code first the infection

     

    External Causes of Morbidity. ICD-10 codes in the range V00-Y99 are not accepted as the primary or first listed diagnosis as they describe the cause of the morbidity, not the condition itself.

     

    Etiology: the cause of the disease

    Sequela: a condition which is the cause of a previous illness

    Morbidity: the condition of being diseased


    Manifestation: a symptom




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